Ipsilateral Fallopian Tube and Ovary Agenesis or Absence? Case Report and Review of the Literature

The unilateral agenesis and/or absence of ipsilateral fallopian tube and ovary (adnexa) is rare and rarely described in the literature. The esteemed incidence is 1:11.240 [1,3]. The etiology is not clear: ipsilateral tubal and ovarian absence could be caused by the torsion of ovarian peduncle before birth or before puberty [2,3]. Adnexa agenesis is always associated to uterine and to urinary apparatus malformations; unilateral agenesis or absence are rarely associated to genital and extragenital malformations. The majority of affected patients has no special symptoms and signs and the diagnosis follows a laparoscopy or a laparotomy performed for different causes. We report the case of young women affected by primary amenorrhea and review the literature regarding adnexal agenesis and/or absence.